ENFERMEDAD DE HAND SCHULLER CHRISTIAN PDF

La histiocitosis de células de Langerhans (HCL) es una enfermedad poco frecuente M.A. TossSurvey of Hand-Schuller- Christian’disease in otolaryngology. Xantomas en paciente con histiocitosis de células de Langerhans y cirrosis de formas crónicas progresivas, como la enfermedad de Hand-Schüller-Christian. Hashimoto-Pritzker disease, a congenital self-healing form; Letterer-Siwe disease, a severe, acute and disseminate form; Hand-Schüller-Christian disease, .

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D ICD – Department of Oral and Maxillofacial Surgery. TI-weighted image with contrast: Int J Dermatol ; Smoking cessation may lead to reversal of changes or evolution to pulmonary fibrosis and pulmonary hypertension.

Introduction Langerhans cell histiocytosis LCH is a disease of unknown etiology, characterized by proliferation of pathological Langerhans cells within different organs Histiocytic sarcoma Langerhans cell sarcoma Interdigitating dendritic cell sarcoma Follicular dendritic cell sarcoma. The lesion was elastic to the touch, painful, and impeded normal upper eyelid movement Fig. Albacete 2 Head of Section. The lesion was resected once again, and the histopathological report revealed LCH.

Hand–Schüller–Christian disease

Langerhans cell histiocytosis, LCH, histiocytosis X, lymphoproliferative disease. In the skull, lesions usually have sharply defined borders with uneven involvement of the inner and outer table. Bone scintigraphy showed pathological focal hypercaptation in the enferemdad of the lesion, the latter resected by means of a combined craniofacial approach.

The soft tissue mass accompanying all osseous lesions can best be seen with CT scan and MRI 3ce latter showing a well-defined area of soft tissue surrounding a focal lesion, with altered bone marrow signal 2. Juvenile xanthogranuloma Hemophagocytic lymphohistiocytosis Erdheim-Chester disease Niemann—Pick disease Sea-blue histiocyte Benign cephalic histiocytosis Generalized eruptive histiocytoma Xanthoma disseminatum Progressive nodular histiocytosis Papular xanthoma Hereditary progressive mucinous cristian Reticulohistiocytosis Multicentric reticulohistiocytosisReticulohistiocytoma Indeterminate cell histiocytosis.

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Four years following surgery, the patient was diagnosed with hypogonadotropic hypogonadism and diabetes insipidus. After adequate workup to determine the extent of the disease, no other lesions were encountered. Revision de la literatura. The overall 5-year survival rate for LCH is approximately MRI of the hips and femur showed isotense lesions on T1-weighted images, which showed enhacement with gadolinium, and high signal areas of bone replacement on T2-weighted images.

CT of the femur soft tissue window. Discussion Hand-Schuller-Christian disease is a chronic disseminated form of histiocytosis X, in which idiopathic non-neoplastic proliferation of histiocytes occurs. There are no controlled studies establishing optimal treatment for LCH 2,7,9, Neoplasm of the immune system.

enfermedad de Hand-Schüller-Christian

Related Bing Images Extra: Proceedings of the Pathological Society of Philadelphia, ee, Nine years post-surgery, there are no signs of recurrence of the lesion. Tumors of the Head and Neck in children. CT of the pelvis soft tissue window: On the orthopantomogram, new cystic lesions were observed in the regions of dental pieces 25, 36 to 37, and 46 to 48, with affectation of these teeth Fig.

Radiotherapy, in doses of 1, to 1, cGys, enferjedad been proposed for non-accessible lesions, for those which compromise vital structures such as the optic nerve, and for recurrence of previously resected lesions 6,9, La histiocitosis de celulas de Langerhans, tambien conocida como sindrome X, granuloma eosinofitico, enfermedad de Letterer-Siwe y enfermedad de Hand-Schutter-Christian es una enfermedad protiferativa que se caracteriza por la acumulacion irregular y localizada de cetutas en cualquier tugar det envermedad 1.

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The lesions may also appear as permeative lesions with ill-defined borders and periosteal reaction. Current insights in a molecular age with emphasis on clinical oral and maxillofacial pathology practice. The radiological image of “floating teeth” is typical of maxillary and mandibular involvement 2,3,5,11,14, Matsushima Y, Baba T.

Hicks J, Flaitz CM. Content is updated monthly with systematic literature reviews and conferences. Large lesions give the appearance of “geographic skull”. Comprehensive management of Head and Neck Tumors. Chrstian advocate surgical treatment of the lesion by means of curettage or biopsy 4,6,7,11,12,14or intralesional injection of corticosteroids enfermedaad, Letterer-Siwe definition of Letterer-Siwe by Medical dictionary https: Infobox medical condition new All stub articles.

Langerhans cell histiocytosis restricted to the oral mucosa.

Langerhans’ cell histiocytosis

Bone scintigraphy showed a single, hypercaptating lesion in the right supraorbital region. Four months following the dw surgery, the patient presented with trismus, swelling and pain in the left upper jaw and in right and left mandibular bodies. To further this end, patients suffering from this disease, particularly those with multiorganic affectation, should be included in clinical trials carried out by the Histiocytosis Society.